Title: Tetralogy of Fallot in a 64-year old untreated woman
- Paulina Wejner-Mik, Maria Krzemińska-Pakuła, Jarosław D. Kasprzak
- Case Reports
- Polish Journal of Cardiology
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- Final page:
- tetralogy of Fallot, adults, three-dimensional echocardiography
Tetralogy of Fallot (ToF) is the most frequent cyanotic congenital cardiac disorder. ToF patients rarely reach an adult age without surgical intervention. We present a case of 64-year-old woman with neonatally diagno-sed untreated tetralogy of Fallot. The functional status of this patient was New York Heart Association (NYHA) class III and the systemie blood pressure was 120/70 mmHg. The hematocrit was 51.4% and the ar-terial partial pressure of oxygen 55.7 mmHg. Electrocardiogram presents atrioventricular błock second degree (Mobitz type), with 42 heart ratę. Two- and three-dimensional echocardiography confirmed the pre-sence of typical tetralogy of Fallot with moderate degree of subvalvular pulmonic stenosis. Three-dimensional study allowed detailed planimetry of VSD.
That long survival time seems to be connected with moderate pulmonary stenosis, average degree of right ventricular hypertrophy and good left ventricular funetion. Sufficient heart ratę in spite of atrioventricular błock coexistence and protective lifestyle can also contribute to unusual longevity for tetralogy of Fallot patient.